Acute Phase Reaction after Femur Fracture in a Child with Griscelli Syndrome.
نویسندگان
چکیده
Griscelli syndrome (GS) is an autosomal recessive disorder that is characterized by partial albinism of the skin and hair shaft. Prompt and early diagnosis is a crucial step for the follow up and management of GS, which would otherwise dramatically decrease the life expectancy of the patients. This case report presents the clinical course of a femoral fracture treated with closed reduction and pelvic-pedal cast, and progression of acute phase reaction during the follow up period.
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ورودعنوان ژورنال:
- Turkish journal of anaesthesiology and reanimation
دوره 42 3 شماره
صفحات -
تاریخ انتشار 2014